31st Annual North American Cystic Fibrosis Conference

Nov 2, 2017 ‐ Nov 4, 2017


The North American Cystic Fibrosis Conference (NACFC) provides a collaborative and educational forum for CF professionals to help advance CF research and care. This annual meeting brings together scientists, clinicians, and caregivers from around the world to discuss and share ideas on the latest advances in CF research, care, and drug development and to exchange ideas about ways to improve the health and quality of life for people with CF.


Sessions

SC06: NTR: CF Nutrition 101 (TICKET REQUIRED)

Nov 1, 2017 3:30pm ‐ Nov 1, 2017 7:30pm

Identification: SC06

This introductory short course on nutrition in CF is designed for healthcare providers who are new to CF. This course will emphasize the role of nutrition in optimizing CF outcomes and the practical application of medical nutrition therapy for CF throughout the lifespan. Specific topics will include: general age-appropriate nutrition recommendations, pediatric feeding behavior, pancreatic enzyme replacement, the CF gut and GI challenges, vitamin and mineral supplementation, pregnancy, CF-related diabetes, and supplemental nutrition therapy. Available educational resources and current evidence-based literature will be provided and reviewed. By the end of the course, participants will have the resources to provide basic nutrition care in CF clinical practice. This class is not intended for advanced nutrition and CF practitioners.

Learning Objectives:

  1. Describe the relationship of weight, growth, BMI, and optimal nutritional status to CF health outcomes.
  2. Summarize GI complications, recommended vitamin and mineral supplementation, and enzyme management throughout the life cycle.
  3. Summarize nutrition challenges and management techniques of adults who have CF including CFRD and pregnancy.

Short Course Leader(s): Short Course Speaker(s):

SC07: PT& RT: Research & Exercise in CF: Where Do We Start? Where Do We Go? (TICKET REQUIRED)

Nov 1, 2017 3:30pm ‐ Nov 1, 2017 7:30pm

Identification: SC07

Exercise is an important functional and prognostic factor. Research in exercise in CF presents a variety of study design challenges, including selection of the patient population, study intervention, outcome measures, and data analysis plan. This short course is designed to provide the participant with the fundamentals needed to conduct research in exercise in CF, culminating in a group design activity- bring your ideas!

Learning Objectives:

  1. Describe the knowledge gap and research question you wish to answer in exercise and physical activity in Cystic Fibrosis.
  2. Identify exercise and physical activity assessment tools and outcome measures needed to answer the research question.
  3. Design a trial with appropriate inclusion and excluision criteria, sample size calculation, and data analysis plan.

Short Course Leader(s): Short Course Speaker(s):

SC08: SW/PSYCH: Positive Parenting Interventions for Common Behavioral Issues in Children With CF (TICKET REQUIRED)

Nov 1, 2017 3:30pm ‐ Nov 1, 2017 7:30pm

Identification: SC08

This course will focus on teaching care providers how to provide empirically-supported parent education on management of common behavioral concerns among children with CF. Topics will include improving cooperation during daily medical cares and at mealtimes, communicating with children and their siblings about CF, screening for the need for behavioral intervention services, and other areas of interest.

Learning Objectives:

  1. Summarize to provide guidance to parents about evidence-based behavioral management strategies to overcome medical regimen adherence barriers and reduce common child behavioral concerns.
  2. Identify parent-child communication challenges and strategies for improving family communication.
  3. Employ knowledge of empirically-supported screening tools to identify children in need of behavioral intervention.

Short Course Leader(s):

SC09:Virtual Improvement Program-Fundamentals (VIP-F3) (TICKET REQUIRED)

Nov 1, 2017 3:30pm ‐ Nov 1, 2017 7:30pm

Identification: SC09

This formal improvement fundamentals course supports CF programs enrolled in the VIP-F3 (Virtual Improvement Program - Fundamentals). The course is​ a highly interactive introduction to the improvement fundamentals, which will have been preceded by 3-4 months of preparatory organization and planning with an assigned CF quality coach. The CFF improvement fundamentals is based on successful improvement in improving care for people with CF, which is enhanced with an electronic learning platform complete with a CF case study. A CF quality coach will support improvement development for 3 months based on the CF program needs following the NACFC short course.

Learning Objectives:

  1. Develop a plan for quality improvement at your CF center through the Dartmouth Microsystem Improvement Curriculum (DMIC) ramp.
  2. Assess current practice (include CF registry data for 5P assessment and improvement measurement); create a draft global statement and create a flowchart.
  3. Describe how to use and display data to understand current clinical practices; identify areas for change and measurement improvement.

Short Course Leader(s):

W01: APP&D: Airway Transport of Ions, Fluid & Mucus in CF

Nov 2, 2017 9:45am ‐ Nov 2, 2017 11:05am

Identification: W01

The coordinated secretion of ions, fluid, & mucin into the airway lumen resulting in effective mucus clearance serves to protect the airways from inhaled particulates & pathogens. When the secretion of ions, fluid, or mucin is dysregulated or cilia function is defective, mucus transport & clearance can fail leading to airway infection & disease. CFTR plays a central role in regulating ion & fluid transport in the airways & defective CFTR function is strongly correlated with dysfunctional mucus transport & clearance. This workshop focuses on how ion, fluid, & mucin secretion are regulated in the airways, how regulation of mucus transport is disrupted in CF airways, & which components of the mucus transport process can be targeted therapeutically to restore defective mucus transport.

Learning Objectives:

  1. Identify the contribution of ion, fluid, & mucin secretion to effective mucus clearance in the airways & why it may fail in CF airways.
  2. Differentiate between the mucin species secreted by the proximal & distal airways & their biological significance.
  3. Evaluate the importance of ion, fluid, &/or mucin secretion as therapeutic targets for enhancing mucus clearance and assess the utility of new in vivo techniques for measuring mucus clearance in humans.

Workshop Chair(s): Workshop Speaker(s):

W02: CFTR: CFTR 2017W02: CFTR: CFTR 2017

Preview Available

W02: CFTR: CFTR 2017

Nov 2, 2017 9:45am ‐ Nov 2, 2017 11:05am

Identification: W02

This workshop focuses on new insights into the biosynthetic pathway of CFTR and highlights recent developments relating to protein structure and function. Additionally, discussions will include evaluation of currently available small molecule-based therapies and their effects on CFTR channel activation across multiple species. Clinical implications of these findings will also be addressed.

Learning Objectives:

  1. Describe novel strategies for the development and functional characterization of CFTR modulators.
  2. Summarize topical advances in CFTR structure and visualization.
  3. Assess efficacy of current CFTR pharmacological correctors and potentiators within various in vitro and in vivo contexts.

Workshop Chair(s): Workshop Speaker(s):

W03: CLIN: Advanced Lung Disease & Transplantation in CF

Nov 2, 2017 9:45am ‐ Nov 2, 2017 11:05am

Identification: W03

This session will provide an overview of the lung transplant process, factors that are associated with better or worse outcome post-transplant and factors that affect the possibility of transplant.

Learning Objectives:

  1. Review factors of CF associated to disease deterioration and outcome post-transplant.
  2. Describe transplant referral for CF in different centers.
  3. Discuss waiting times and lung allocation according to age

Workshop Chair(s):
  • Cecilia Chaparro, M.D., MSc., Respirologist, University of Toronto
  • Erin Lowery, M.D., M.S., Assistant Professor of Medicine and Pediatrics
Workshop Speaker(s):

W04: CLIN: Endocrine WorkshopW04: CLIN: Endocrine Workshop

Preview Available

W04: CLIN: Endocrine Workshop

Nov 2, 2017 9:45am ‐ Nov 2, 2017 11:05am

Identification: W04

Presentation of abstracts on the pathophysiology of cystic fibrosis related diabetes (CFRD), growth in CF children, and influences on bone health.

Learning Objectives:

  1. Describe the pathophysiology of CFRD and the association of type 2 diabetes mellitus genes.
  2. Compare growth in CF rats versus CF infants.
  3. Describe bone accrual in pancreatic insufficient CF children.

Workshop Chair(s): Workshop Speaker(s):

W05: CLIN: Evolving Concepts of Quality Improvement

Nov 2, 2017 9:45am ‐ Nov 2, 2017 11:05am

Identification: W05

This workshop will provide attendees with an overview of innovative QI work in the CF community.

Learning Objectives:

  1. Describe innovative QI techniques to improve patient outcomes.
  2. Identify ways to engage patients and families in QI work.
  3. Discuss ways participants might implement similar innovations at their care center.

Workshop Chair(s): Workshop Speaker(s):

W06: INF/MIC: Pathogenesis of Infection

Nov 2, 2017 9:45am ‐ Nov 2, 2017 11:05am

Identification: W06

Chronic lung infections and the associated inflammation are the leading cause of morbidity and mortality in cystic fibrosis (CF) patients. Thus, the continuing study of microbial pathogens found in the CF airways and how they interact with the host is of great importance. The purpose of this workshop is to highlight novel approaches to allow a greater understanding of primary and emerging pathogens in CF patients.

Learning Objectives:

  1. Describe important changes acquired in the adaptation of pathogens in the CF lung.
  2. Discuss major pathogens in CF airways and how to identify them.
  3. Recall the clinical importance of microbial pathogenesis as it relates to CF disease.

Workshop Chair(s): Workshop Speaker(s):
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