32nd Annual North American Cystic Fibrosis Conference

Oct 18, 2018 ‐ Oct 20, 2018



Sessions

SC04--CLIN-INF/MIC-NRS: Optimization of Antibiotics in Emerging Pathogens

Oct 17, 2018 3:30pm ‐ Oct 17, 2018 7:30pm

Experts will discuss the use of oral, inhaled, and intravenous antibiotics for challenging pathogens that are encountered in CF: MRSA, Pulmonary Non-tuberculous mycobacteria (NTM), multi-drug resistant (MDR) Pseudomonas aeruginosa, B. cepacia complex, Stenotrophomonas maltophilia, and Achromobacter species. In addition, we will discuss the diagnosis and management of allergic bronchopulmonary aspergillosis (ABPA). The session will be practical with a focus on the approach to actual CF patients and the nuances of individual cases will be discussed. Handouts will be provided with dosing and clinical scenarios to consider oral, inhaled, and intravenous antibiotics for these pathogens.

Learning Objectives:

  • Create an approach to asymptomatic, new MRSA infection as well as the outpatient management of chronic symptomatic MRSA infection.
  • Explain the importance of multiple antibiotics as well as discuss options and approach for the treatment of MDR gram negative infections.
  • Design & assess therapeutic options of pulmonary NTM and ABPA infections.

Short Course Leader(s): Short Course Speaker(s):

SC05--NRS: Advanced Pharmacology for the CF Provider

Oct 17, 2018 3:30pm ‐ Oct 17, 2018 7:30pm

This session is designed to examine the practice and evidence behind pharmacological management for CF-related arthropathy, sinus disease, constipation/DIOS and GERD. It will include both inpatient and outpatient management approaches and is suitable for clinicians (physicians, pharmacists, and mid-level providers (PA's, APN, or NP)) caring for individuals with CF.

Learning Objectives:

  • Identify potential pharmacological management options in the treatment of CF-related sinus disease.
  • Compare/contrast approaches to management of CF-related GI manifestations of GERD, DIOS, and constipation.
  • Describe potential treatment options for CF-related arthropathy.

Note: Speaker Bradford Woodworth's presentation was not recorded at his request. 

Short Course Leader(s): Short Course Speaker(s):

SC06--NTR: Advanced Nutrition iconSC06--NTR: Advanced Nutrition

Preview Available

SC06--NTR: Advanced Nutrition

Oct 17, 2018 3:30pm ‐ Oct 17, 2018 7:30pm

This short course, focusing on nutrition, is designed for dietitians/nutritionists and other CF care team members who possess basic experience in CF nutrition and are interested in expanding their knowledge of nutritional concepts and practical applications. Topics covered may include pregnancy, transplant, appetite stimulants, enzymes, tube feeding, vitamins and minerals, diabetes, and infant care. Information presented will incorporate current guidelines, new research, practical skills, and case studies. Knowledge gained during this course will help improve the quality of nutrition care delivered to CF patients.

Learning Objectives:

  • Assess nutrition status of individuals with CF across the lifespan.
  • Explain the unique nutrient needs of individuals with CF.
  • Identify areas of their own nutrition practice for improvement.

Short Course Leader(s):

SC07--PT&RT: Getting to the Core of Continence for Adults & Children With CF: New Strategies for Physical Therapists

Oct 17, 2018 3:30pm ‐ Oct 17, 2018 7:30pm

This presentation was not recorded at the request of the presenters.

The breathing and postural demands of the trunk muscles are often compromised in people with cystic fibrosis, leading to secondary impairments such as postural deficits, stress urinary incontinence (SUI), pain and other functional impairments. This hands-on course will introduce clinicians to an innovative clinical model that incorporates neuromuscular-based core recruitment strategy, driven by external cueing of both the pelvic floor and the diaphragm. Linking the pelvic floor and diaphragm to work as a team, will equip participants to move beyond basic pelvic floor muscle strengthening exercises for SUI to simultaneously address proximal control, continence, breathing mechanics, functional impairments, pain and more through a dynamic foundation of support.

Learning Objectives:

  • Describe the dynamic core muscles, inclusive of the diaphragm and pelvic floor, and their intertwined role in breathing, continence, proximal control and functional movements.
  • Demonstrate how to assess alignment and function of the dynamic core system (even during a busy clinic visit).
  • Discuss simple intervention strategies appropriate for pediatrics and adults with CF to minimize secondary impairments.

Short Course Leader(s):

SC08-SW/PSYCH- NTR-CLIN: Dynamic Interactions Between CF Teams & Transplant Teams to Improve Referral Processes & Promote Outcomes

Oct 17, 2018 3:30pm ‐ Oct 17, 2018 7:30pm

Despite therapeutic advances and increasing life expectancy in the CF community, lung transplantation can be a treatment option for select persons with CF and advanced lung disease. The decision to pursue transplantation is a complex balance of individual choice, physician judgment of medical indication and an individual's candidacy; criteria established by transplant programs and often not fully appreciated by CF programs. This course provides a framework for exploring dynamics of referrals while sustaining the individual's commitment and intention to achieve their desired goal. We will address how partnerships between CF and Transplant teams can afford more transplant opportunities and explore emotional turmoil that can be experienced during the pursuit of new lungs. With exclusive viewing of a personal documentary, 'Fight Like a Boss', a CF adult's transplant journey, attendees will discuss mental health challenges and develop strategies to enhance outcomes.

Learning Objectives:

  • Review the current state-of-the-art in CF Care that impacts the timing and referral of persons with CF for consideration of transplant.
  • Explore best practices from the perspective of CF teams and transplant teams with objective to enhance understanding of the transplant requirements which encourage partnership with patients and families across the transplant spectrum.
  • Identify strategies and interventions that optimally support teams, caregivers and patient intention to achieve transplantation.

Short Course Leader(s): Short Course Speaker(s):

SC09--U&C: Tips & Tricks Navigating Insurance, Benefits, & the Specialty Pharmacy

Oct 17, 2018 3:30pm ‐ Oct 17, 2018 7:30pm

The session will arm clinicians with information to help them in conversations with their patients regarding insurance coverage and access to therapies with an emphasis on assisting patients that have Medicare coverage. The session will also help clinicians in understanding the role of the specialty pharmacy and pharmacists in a complex patchwork of insurance and benefits.

Learning Objectives:

  • Describe strategies for navigating common insurance issues.
  • Identify programs that provide financial assistance for CF medications and care.
  • Define medicare benefits and medicare related challenges in the CF population.

Short Course Leader(s): Short Course Speaker(s):

W01--APP&D-GMS: Airway Transport of Ions, Fluid & Mucus

Oct 18, 2018 9:45am ‐ Oct 18, 2018 11:05am

This session will discuss recent developments in fluid, ion, and mucus transport, with an emphasis on the role of abnormal cells and gland function.

Learning Objectives:

  • Define the role of abnormal cell and gland secretions on mucus and fluid transport.
  • List the properties of mucin and mucus and how these may affect transport.
  • Recall the mechanisms by which mucins clear the airway, and implications of pathology.

Workshop Chair(s): Workshop Speaker(s):

W02--CFTR: CFTR 2018 iconW02--CFTR: CFTR 2018

Preview Available

W02--CFTR: CFTR 2018

Oct 18, 2018 9:45am ‐ Oct 18, 2018 11:05am

This workshop will initially discuss how insights into mechanisms regulating CFTR biosynthesis can help identify new targets for therapeutic intervention. A new tool for detecting plasma membrane CFTR, which could be used in high-throughput setting, will be also presented. The section will end with discussing how the newly resolved cryo-EM CFTR structures may enable structure-based drug design.

Learning Objectives:

  • Define folding and misfolding of CFTR.
  • Describe how the CFTR biosynthetic pathway can be targeted to correct several CFTR mutation classes.
  • Evaluate new approaches for assessing CFTR plasma membrane abundance and helping to design new CFTR modulators.

Note: Speaker Yunjie Huang's presentation was not recorded at his request. 

Workshop Chair(s): Workshop Speaker(s):

W03--CLIN: Gastroenterology & Hepatology

Oct 18, 2018 9:45am ‐ Oct 18, 2018 11:05am

This session will highlight recent research studying assessment and treatment of the gastrointestinal and liver manifestations of cystic fibrosis. The session will focus on: 1) assessment of common CF gastrointestinal problems, including development of innovative therapies; and 2) clinical research to better understand manifestations of and outcomes for CF-related liver disease.

Learning Objectives:

  • Recall the definition of CF-related liver disease and appraise the associations of CF-related liver disease with insulin resistance and mortality.
  • Examine methods for novel drug development and application in constipation in CF.
  • Assess esophageal impedance and gut microbiota dysbiosis in pediatric patients with CF.

Workshop Chair(s): Workshop Speaker(s):

W04--CLIN: Epidemiology & Health Services Research

Oct 18, 2018 9:45am ‐ Oct 18, 2018 11:05am

This workshop will examine the impact of mental health and treatment on lung function decline and risk of future exacerbations. In addition, the interpretations of conditional survival and reproducibility of FEVwill be described.

Learning Objectives:

  • Describe the impact of depression, mucolytics, and antibiotics on lung function decline in the US and Europe.
  • Identify a clinically meaningful change in FEVfor CF patients.
  • Review the interpretation of conditional survival and the factors that are associated with an increased risk of death before age 30.

Workshop Chair(s): Speaker(s): Workshop Chair(s): Workshop Speaker(s):
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