Nutrition, weight & BMI are a focus at every CF clinic visit for children, families & the CF care team. Meal time can be stressful for many patients & their families if they are worried about weight & growth. This course will discuss building & maintaining a positive feeding relationship, from infancy through childhood, using child development, nutrition recommendations & the latest research.
Identify & discuss behaviors that can promote positive attachment between caregivers & infants to promote a positive feeding environment.
Discuss areas for anticipatory guidance & support of caregivers to meet the special nutrition needs of children with CF.
Discuss ways to help families with calorie intake goal setting & tracking of progress.
This short course will describe the core knowledge & skills research coordinators need to manage the daily activities of a research study while ensuring research subject safety . Organizational strategies will be discussed. Clinical trial outcome measures specific to CF will be discussed & a patient's perspective on clinical trial participation will be presented.
Identify common comorbidities seen in medical histories of patients with CF & medications used to treat them.
Describe clinical trial outcome measures specific to CF.
Employ knowledge gained & identify tools to organize study documents, manage study visits & documentation of data to ensure compliance with GCP.
The overall goal of this short course to provide CF care providers with the skills & knowledge necessary to provide advanced therapy via an interactive discussion & case-based format. This short course will address the following therapeutic areas: 1. CFTR Modulators & Novel Therapies; 2. Advanced Drug Delivery for an Acute Pulmonary Exacerbation; 3. Nontuberculous Mycobacteria; & 4. ABPA.
Describe & evaluate CFTR modulators & new/novel therapies for CF.
Discuss & design an evidence-supported continuous/extended infusion beta-lactams & inhaled antibiotics regimen for treating an acute pulmonary exacerbation.
Create & assess therapeutic options to treat NTM & ABPA infections in CF.
New guidelines from the CF Foundation & European CF Society recommend screening & treatment for depression & anxiety. This course will teach practitioners what they need to know about using psychotropic medication in individuals with CF.
Assess anxiety & depression symptoms in individuals with CF before prescribing medication.
Review how to use medications recommended by the CFF/ECFS to treat anxiety & depression in individuals with CF.
Identify CF-specific factors that may influence the use of psychotropic medication.
This course will include the following topics: age-appropriate recommendations, pediatric feeding behavior, pancreatic enzyme replacement, GI challenges, vitamin/mineral supplementation, pregnancy, CF-related diabetes, & end-of-life nutrition. Available resources will be reviewed as well as current evidence-based literature.
Describe the relationship of weight, growth, body mass & optimal nutritional status to CF health outcomes.
Summarize GI challenges, recommended vitamin & mineral supplementation & enzyme management throughout the life cycle.
Summarize nutrition challenges & management techniques of adults who have CF including CF-related diabetes & pregnancy.
This short course is intended for clinicians who have had some exposure to CBT for anxiety and/or depression interested in building on their comfort level & skill to integrate CBT into their practices. The focus will be on CBT interventions that can be introduced in brief sessions with patients & in busy clinic settings. There will be opportunities for hands-on & interactive learning.
Practice assessment & case conceptualization using a CBT model.
Practice several essential CBT techniques for the treatment of anxiety & depression.
Identify potential barriers & solutions to the integration of CBT into clinical practice.
In this course different types of current evidence-based modern ACTs will be presented, including the Active Cycle of Breathing Technique; Autogenic Drainage; Positive Expiratory Pressure (PEP); Oscillating PEP & external oscillating devices. Also the rationale for techniques, how they affect the pathophysiology of CF together with indications & contraindications & precautions will be discussed.
Discuss the different types of evidence-based Modern Airway Clearance Techniques currently available.
Describe selection of individiualized airway clearance techniques & situations when they are contraindicated.
Discuss the importance of exercise & adherence to therapy across the lifespan in CF.
This comprehensive short course will provide didactic & applied education on practical improvement measurement skills for rapid cycle systems performance improvement in CF care, including: (1) defining measures; (2) linking measures to aims, improvement (change) ideas & the data collection plan; (3) creating run charts, SPC charts; & performance dashboards; & (4) utilizing the CF registry.
Demonstrate how to link operationally defined measures to improvement aims & change ideas.
Demonstrate how to create a basic data collection plan.
Apply measurement skills to create & interpret run charts, XmR charts, p charts & performance dashboards.
This workshop is designed to address the cutting-edge research questions to get insights into CFTR biology. It will focus on mutation-specific protein expression, folding, stability & function especially, but not limited for researchers or anyone who is interested in expanding their knowledge on CFTR structure.
Evaluate the current state of mutation-specific therapies & correction of CFTR variants.
Describe the role of interdomain interactions on expression, folding, stability & function of CFTR mutations.
Identify key modulators that correct trafficking & functional defects.
This workshop will introduce two rodent models of CF (Î”F508 CFTR rat & a CF mouse expressing human CFTR) & provide new insights into biliary & respiratory CF disease from experiments performed using CF mouse, ferret or pig models. Particular emphasis will be given to evidence demonstrating infection- & inflammation-independent defects in CF airway function.
Summarize the advantages/disadvantages of new CF rodent models (the Î”F508 CFTR rat & human CFTR expressing mouse).
Explain implications of defective biliary ATP release in CF mice & age-dependent defects in CF ferret alveolar macrophages.
Summarize implications of sterile bronchiectasis in CF ferret lungs & inflammation-independent smooth muscle dysfunction in CF pig airways.