This session is designed to examine the practice and evidence behind complex case scenarios in the pharmacological care of persons with CF. This will be a case-based session discussing various topics including: pharmacological management for pre- and post-transplant patients with regards to CFTR modulators, fungal-related conditions such as allergic bronchopulmonary aspergillosis with biologic agents, and reproductive health. It will include both inpatient and outpatient considerations and is suitable for clinicians (physicians, pharmacists, and mid-level providers (PA's, APN, or NP)) caring for individuals with CF.
Discuss the use of CFTR modulators in pre- and post- liver and lung transplant settings.
Describe current experience in the use of biologics in treatment of CF-related allergic bronchopulmonary aspergillosis and identify possible scenarios to consider less common fungal infections such as coccidioidomycosis.
Describe current challenges and approaches to care with regards to reproductive health of persons with CF.
Note: Speaker Hanna Phan's presentation was not recorded at her request.
The overall goal of this short course is to provide clinicians with knowledge and skills to provide advanced therapy for treatment of CF infection and inflammation. The course will utilize lecture, interactive discussion, and case-based formats.
The following topics will be addressed:
Treatment of Pseudomonal and Non-Pseudomonal Pulmonary Infections with Inhaled antibiotics
Reducing Inflammation in CF Lungs, current and future strategies.
Describe inhaled therapies prescribed to treat CF Pulmonary Exacerbations caused by Pseudomonas.
Formulate management strategies for treatment of sino-pulmonary exacerbations caused by non-Pseudomonas pathogens.
Identify therapies targeting CF lung inflammation and discuss the risks and benefits associated with the use of steroids in patients with CF.
The overall goal of this short course is to provide CF care providers with the skills and knowledge on the optimal management of pulmonary exacerbations. The focus will be on reviewing current guidelines, goals of treatment of a pulmonary exacerbation, choice of antibiotics, dosing and duration of antibiotics, considerations for home versus hospital treatment, effective airway clearance during an exacerbation, and treatment of severe pulmonary exacerbations. Speakers include Pediatric Pulmonologists, Adult Pulmonologists, Physical Therapist, and a Pharmacist. The session will focus on the approach to actual CF patients, and the nuances of individual cases will be discussed. Handouts will be provided with recommended dosing of antibiotics and clinical scenarios.
Describe the basis for consensus guidelines for treatment of pulmonary exacerbations.
Formulate an approach for treatment of pulmonary exacerbations based on guidelines and current practices.
Design and assess pulmonary exacerbation treatment regimens for complicated infections and/or sick patients.
Outcomes for people with CF continue to improve with exciting new therapies. These therapies are expected to improve outcomes even further, yet, we know that some people with CF will continue to progress to advanced lung disease and require special attention. This course will educate CF care teams about the advanced lung disease initiative. This includes palliative care, how to manage advanced lung disease, lung transplant referral, and post lung transplant care. These topics will be highlighted through the introduction of toolkits, case studies, an example of a shared care model through the transplant journey, and a review of recent and upcoming clinical care guidelines.
Review the complex medical and psychosocial care needs of individuals with advanced CF lung disease.
Define existing and upcoming guidelines for the clinical care of individuals with advanced CF lung disease including general CF care, palliative care, referral for lung transplantation, and post-lung transplant care.
Discuss the roles of CF care team members and effective partnerships with other health care providers when caring for individuals with advanced CF lung disease.
The role of the physical therapist in CF care has evolved in recent years. Traditionally providers of airway clearance, PTs are now assessing and treating multiple body systems and have an increasing presence in the CF clinic. The goal of this course is to provide PTs and PTAs with a breadth of assessment tools to be used during a multidisciplinary CF clinic visit. This course will address topics such as pediatric development, vestibular hypo-function and pelvic health. Postural alignment, exercise, and manual techniques will be reviewed. Participants will also learn the importance of including basic airway clearance techniques into their PT sessions to optimize outcomes. Evidence-based practice, case studies and practical skills will be incorporated throughout the course. Target Audience: Physical Therapists and Physical Therapy Assistants.
Identify common secondary impairments seen in people with cystic fibrosis, such as: development delay, postural dysfunction, vestibular hypo-function and pelvic floor dysfunction.
Demonstrate how to efficiently assess these multiple body systems.
Describe simple intervention strategies to address impairments noted during CF clinic assessments.
The session will arm clinicians with information to help them navigate and understand the financial burden people with CF and their families experience. As the treatment plans can be complicated and with the anticipation of the 'triple-combo', care center clinicians will need to be mindful of the financial burden families have related to medical expenses and social determinants of health and how these burdens impact decisions about their health care. This course will provide real, practical tips for addressing out of network needs, navigating appeals, trouble shooting, comparing health plans and the importance of people with CF having the best health insurance coverage available to them.
Describe strategies for navigating common insurance issues.
Identify programs that provide financial assistance for CF medications and care.
Summarize financial burdens and challenges in the CF population.
This course is appropriate for physicians, physician assistants, nurses, nurse practitioners, dietitians, pharmacists, diabetes educators, and other health care professionals who care for patients with CF and cystic fibrosis related diabetes (CFRD). The course will utilize an interactive case based approach to review the diagnostic and treatment strategies for managing CFRD. This course will cover the general principles of nutritional and pharmacological therapy and use of new technology including ambulatory insulin pump and continuous glucose monitoring in management of CFRD. Faculty will discuss clinical scenarios and provide take home practical patient management strategies to improve quality of care of patients with CFRD.
Define where to access the guidelines for Cystic Fibrosis Related Diabetes Mellitus.
Define why we screen for and treat Cystic Fibrosis Related Diabetes Mellitus; and treatment options.
Summarize some of the barriers for effective screening and treatment for CFRD; and potential solutions.
This short course will focus on the basics of CF nutrition. It is designed for dietitians who are new to CF or as a review for other practitioners. Topics will include nutrition assessment, nutrition needs through the lifespan (infancy to adult), pediatric feeding behavior, enteral tube feeds, pancreatic enzyme replacement therapy, GI challenges, vitamin/mineral supplementation, CF-related diabetes, and nutrition in advanced CF. Available resources will be reviewed as well as current evidenced-based literature.
Describe the nutrition goals and interventions for individuals with Cystic Fibrosis from infancy through adulthood.
Review enzyme management and vitamin supplementation for individuals with pancreatic insufficiency and discuss other GI challenges.
Explain the extra-pulmonary complications associated with CF.
This special class is designed for mental health providers who are interested in learning more about how Acceptance and Commitment Therapy (ACT) can be used clinically to promote valued living for individuals with CF and their support systems, including CF team members. The short course will include education about the theoretical foundation of ACT, research findings using ACT with CF and other populations, and its relationship to other forms of psychotherapy. ACT is a third wave behavior therapy where therapists and clients actively engage in behavior change. The majority of the course time will focus on trying out ACT-consistent strategies, identifying clinically relevant ACT targets, and where to obtain ACT training.
Summarize the theoretical underpinnings of Acceptance and Commitment Therapy and how theory informs the clinical approach to treatment delivery.
Relate how changing the relationships between thoughts, emotions, and behaviors can facilitate living a valued life.
Identify resources to facilitate future clinical practice.