Research continues to validate the importance of a well- nourished state as related to outcomes in cystic fibrosis as well as best nutrition practices. This session will review current topics in nutrition and cystic fibrosis including improvement in weight and pulmonary function outcome with Ivacaftor treatment. Also presented will be specific intake data as well as recommendations leading to best feeding practices for children of all ages. Use and incidence of adverse effects of proton pump inhibitors in cystic fibrosis will also be presented.
Compare rate of weight gain in infants with CF who are exclusively breast fed to those receiving other infant feeding modalities and to quantify the intake of core and non-core foods consumed to meet caloric requirements.
Evaluate the effect of Ivacaftor on the weight status and pulmonary function on individuals with CF and to examine the macronutrient intake of preschoolers diagnosed with CF.
Identify the potential adverse events associated with use of PPIs , and be able to describe dosing and prevalence of use.