This workshop will review clinical research on the evaluation and treatment of pulmonary manifestations of cystic fibrosis. The research presented will include predictors of disease severity and response to treatment as well as a novel imaging technique utilizing magnetic resonance. The session will also explore how the addition of therapies such as hypertonic saline and ivacaftor may benefit cystic fibrosis patients.
Demonstrate an understanding of the role of 3D ultrashort Echo time MRI in the assessment of air trapping in CF.
Discuss the standardized treatment of pulmonary exacerbations and the variables which predict response to antibiotic treatment, as well as the association between hemoptysis and severity of disease.
Identify the clinical outcomes associated with the combined use of hypertonic saline and RHDNAse and a proposed mechanism of early spirometric improvement with the use of ivacaftor.
Assistant Professor of Pediatrics,
Vanderbilt University Medical Center
Director, Adult CF and Co-Director, GRU CF Center,
Georgia Regents Univ